SEORANG PENDERITA HEMOFILIA RINGAN DENGAN PERDARAHAN MASIF

Abstract

Haemophilia A is the most common of the hereditary clotting factor deficiencies, which have defect of absence or low
level factor VIII in the plasma. It is a X-linked recessive inheritance disease, with incidence approximately 1 per 10.000 male
birth. In the middle of the year 2001,it were reported 314 cases in Indonesia. The clinical features of the bleeding may be shown
many various severity, and classified into mild, moderate and severe disease. The clinical severity of the disease correlates with
the extent of the factor VIII deficiencies. Diagnostic confirm by specific clinical features, there is a history of the bleeding in the
family, and laboratorium examination to measure the factor VIII level in the plasma. We reported a case, male, 46 years old,
Balinese, reffered from private hospital with complaining profuse bloody vomiting and blackish stool and has been done blood
transfusion for 15 bags, with history of haemophilia confirmed. The history of bleeding before classified patients into a mild
disease, but in the present the patient suffered from chronic liver disease and erosive gastritis, that can lead patients has more
profuse bleeding. A good respons shown by giving the transfusion of the cryopresipitate and packed red cell.