PEUTZ JEGHERS SYNDROME PRESENTING WITH ACUTE INTESTINAL OBSTRUCTION: A RARE CASE REPORT WITH REVIEW OF LITERATURES

  • P. K. Hota Professor of Surgery, Department of General Surgery, Mamata Medical College Khammam, Telangana India Pin-507002
  • G. Narasimha Reddy Resident in Surgery, Department of General Surgery, Mamata Medical College Khammam, Telangana India Pin-507002
  • G. Rajasekhar Resident in Surgery, Department of General Surgery, Mamata Medical College Khammam, Telangana India Pin-507002
  • C. Nalini Mohan Assistant Professor, Department of Pathology, Mamata medical College Khammam, Telangana India Pin-507002

Abstract

Background: Peutz-Jeghers syndrome is a rare genetic disorder presenting in young age with mucocutaneous pigmentation and hamartomatous polyposis. Method: We report a case of PeutzJeghers syndrome in a 16 year old boy presenting with acute intestinal obstruction. Results: Imaging studies revealed intussusception. He had mucocutaneous pigmentation and multiple hamartomatous polyps which were diagnosed histologically. The unusual presentation of the case and its successful management has prompted us to report the case with literature review.